Polysplenia syndrome associated to neonatal hepatitis
نویسندگان
چکیده
منابع مشابه
Aortic pseudocoarctation associated with polysplenia/heterotaxy syndrome.
Polysplenia/heterotaxy syndrome is a rare congenital disorder associated with a wide spectrum of anomalies in various organ systems. Although anomalies of the cardiovascular system are common in this syndrome, the authors report a rare case of polysplenia syndrome associated with aortic pseudocoarctation, which to our knowledge has never been reported.
متن کاملHeterotaxia associated with polysplenia.
To cite: Gunes Tatar I, Ergun O, Altunoglu H, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2014-206358 DESCRIPTION A 31-year-old man underwent abdominal CT for blunt abdominal trauma. CT scan demonstrated cardiac apex (figure 1A), stomach (figure 1B, C) and multiple splenic nodules situated on the left of the midsagittal plane; liver and inferior vena c...
متن کاملPolysplenia syndrome with preduodenal portal vein
Polysplenia syndrome is a heterogeneous disease that primarily affects the asymmetric organs, including the heart, lungs and bronchi, liver, intestines, and spleen [1]. It manifests mainly in childhood, 40% of the patients reach 2 years of age and the majority dies before 5 years of the age due to cardiac anomalies [2]. 5-10% of the patients lack cardiac involvement, which allows them to reach ...
متن کاملPolysplenia syndrome - a rare case report
The aim of this study is to report a case of polysplenia syndrome observed in an 1 1/2 yr. old male patient who came for CT thorax for preoperative evaluation of congenital heart disease. There was partial anomalous pulmonary venous drainage – right lung was draining into right atrium and left lung into left atrium. The IVC was interrupted and venous return was via the continuation of enlarged ...
متن کاملCongenital Cardiac Disease Associated with Polysplenia
The well-recognized association of congenital cardiac disease with asplenia has been termed "bilateral right-sidedness" or dextro-isomerism, since the spleen is absent, the liver is symmetrical, and each lung has three lobes and an epiarterial bronchus. In a study of pathological material from 12 patients with congenital cardiac disease associated with multiple spleens (as contrasted to accesso...
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ژورنال
عنوان ژورنال: Jornal de Pediatria
سال: 1998
ISSN: 0021-7557
DOI: 10.2223/jped.413